Date published: 2025-9-8

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PDC-E2 抗体 (C-9): sc-271352

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说明书
  • PDC-E2抗体(C-9)是小鼠单克隆IgG1 κ, 在3篇文献中引用,规格为200 µg/ml
  • 针对氨基酸231-390的图谱,在PDC-E2的内部区域,human起源
  • 推荐用于 mouse, rat 和 human 来源的PDC-E2 WB, IP, IF 和 ELISA检测
  • m-IgG Fc BP-HRP1 BP-HRP">m-IgG1 BP-HRPm-IgGκ BP-HRP是PDC-E2 Antibody (C-9) 适用于 WB 应用。 的首选辅助检测试剂。这些试剂现与PDC-E2 Antibody (C-9) 打包提供(请参阅下面的订购信息)。

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関連項目

原发性胆汁性肝硬化(PBC)是一种慢性、破坏性的自身免疫性肝病,其特征是患者血清中存在抗线粒体自身抗体,以及T细胞介导的小型肝内胆管胆管上皮细胞的破坏。患者血清的特征是针对线粒体抗原的自身抗体的高频率(大于95%),该抗原被鉴定为丙酮酸脱氢酶多酶复合物(PDC-E2)的E2组分。PDC-E2包含氨基末端带脂酰基的域和羧基末端催化域。人类序列保留了带脂酰基位点的Glu-Thr-Asp-Lys-Ala基序。免疫印迹揭示了PDC-E2蛋白的两种构象可变形式。自身抗原的免疫显性自身表位对应于内脂酰基域。发现大量无症状患者对PDC-E2有抗体,这些患者患原发性胆汁性肝硬化的风险很高。

仅限研究使用。不适用于诊断和治疗用途。

Alexa Fluor® 是Molecular Probes Inc., OR., USA的商标

LI-COR®和 Odyssey® 是LI-COR Biosciences的注册商标

PDC-E2 抗体 (C-9) 参考文献:

  1. 人类PDC-E2 163-176肽的模拟肽,原发性胆汁性肝硬化的免疫优势T细胞表位。  |  Shimoda, S., et al. 2000. Hepatology. 31: 1212-6. PMID: 10827144
  2. 对原发性胆汁性肝硬化免疫优势自身抗原PDC-E2 163-176肽有反应的T细胞的精细特异性:对分子模拟和线粒体自身抗原交叉识别的影响。  |  Shigematsu, H., et al. 2000. Hepatology. 32: 901-9. PMID: 11050037
  3. 原发性胆汁性肝硬化患者体内PDC-E2上HLA-A0201限制性CD8 T细胞表位的综合图谱。  |  Matsumura, S., et al. 2002. Hepatology. 36: 1125-34. PMID: 12395322
  4. 原发性胆汁性肝硬化免疫优势自身抗原PDC-E2的人单克隆抗体的表征和抗原表位图谱。  |  Leung, PS., et al. 1992. J Autoimmun. 5: 703-18. PMID: 1283300
  5. 异基因造血干细胞移植后血液系统恶性肿瘤患者和原发性胆汁性肝硬化患者体内PDC-E2抗体的差异表位图谱。  |  Bellucci, R., et al. 2007. Blood. 109: 2001-7. PMID: 17068145
  6. AMA阴性原发性胆汁性肝硬化中CD4 T细胞对线粒体自身抗原PDC-E2的自身反应性。  |  Shimoda, S., et al. 2008. J Autoimmun. 31: 110-5. PMID: 18644699
  7. 原发性胆汁性肝硬化患者体内针对PDC-E2和胆管上皮细胞的组合人类自身抗体的异质性。  |  Cha, S., et al. 1994. Hepatology. 20: 574-83. PMID: 7521314
  8. 对原发性胆汁性肝硬化患者HLA-DR53背景下对人类PDC-E2 163-176肽反应的T细胞克隆的T细胞受体β进行分析。  |  Ichiki, Y., et al. 1997. Hepatology. 26: 728-33. PMID: 9303504
  9. 原发性胆汁性肝硬化患者单克隆IgG和IgM抗PDC-E2/X抗体组的免疫遗传学分析。  |  Thomson, RK., et al. 1998. J Hepatol. 28: 582-94. PMID: 9566826
  10. 原发性胆汁性肝硬化淋巴结诱导的胆管上皮细胞丙酮酸脱氢酶复合物PDC-E2的表达。  |  Sadamoto, T., et al. 1998. Lancet. 352: 1595-6. PMID: 9843108

订购信息

产品名称产品编号规格价格数量收藏夹

PDC-E2 抗体 (C-9)

sc-271352
200 µg/ml
RMB2377.00

PDC-E2 (C-9): m-IgG Fc BP-HRP 套装

sc-537620
200 µg Ab; 10 µg BP
RMB2662.00

PDC-E2 (C-9): m-IgGκ BP-HRP 套装

sc-534937
200 µg Ab; 40 µg BP
RMB2662.00

PDC-E2 (C-9): m-IgG1 BP-HRP 套装

sc-545264
200 µg Ab; 20 µg BP
RMB2662.00

I need to use an antibody to detect the protein in samples of monkey origin. Do you know if sc-271352: PDC-E2 (C-9) mouse monoclonal antibody will work?

Asked by: Trav11
Please contact our Technical Service Department and we would be happy to perform sequence analysis and review our data to answer any questions you may have about additional species reactivity.
Answered by: Technical Support
Date published: 2017-03-06
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Rated 5 out of 5 by from Great Western Blot data of PDCGreat Western Blot data of PDC-E2 expression in non-transfected 293T, human PDC-E2 transfected 293T and HeLa whole cell lysates. -SCBT QC
Date published: 2015-02-17
Rated 5 out of 5 by from Great Western Blot data of PDCGreat Western Blot data of PDC-E2 expression in KNRK and Caki-1 whole cell lysates and mouse liver, rat kidney and mouse heart tissue extracts. -SCBT QC
Date published: 2013-08-20
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PDC-E2 抗体 (C-9) is rated 5.0 out of 5 by 2.
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