Date published: 2025-9-8

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KCNQ2 抗体 (E-6): sc-365114

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说明书
  • KCNQ2抗体(E-6)是小鼠单克隆IgG2b (kappa轻链),规格为200 µg/ml
  • 免疫原氨基酸序列641-780位于human物种的KCNQ2的C-terminus附近
  • 推荐用于 mouse, rat 和 human 来源的KCNQ2 WB, IP, IF 和 ELISA检测
  • 目前,我们还没有完成KCNQ2 抗体 (E-6)的首选二抗检测试剂的鉴定。这项工作正在进行中。

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    関連項目

    癫痫影响着世界上约0.5%的人口,并且具有很大的遗传成分。癫痫是由中枢神经系统的电过度兴奋引起的。钾通道是电信号的重要调节因子,决定着各种神经元的放电特性和反应性。良性家族性新生儿惊厥(BFNC)是一种婴儿期常染色体显性遗传癫痫,已被证明是由KCNQ2或KCNQ3钾通道基因突变引起的。KCNQ2和KCNQ3是电压门控钾通道蛋白,具有六个假定的跨膜结构域。这两种蛋白质在大脑内分布广泛,表达模式在很大程度上重叠。

    仅限研究使用。不适用于诊断和治疗用途。

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    KCNQ2 抗体 (E-6) 参考文献:

    1. 人类KCNQ2通道配体激活的分子基础。  |  Li, X., et al. 2021. Cell Res. 31: 52-61. PMID: 32884139
    2. 在KCNQ2-DEE抗癫痫药物临床试验中捕捉癫痫发作。  |  Millichap, JJ., et al. 2021. Epilepsia Open. 6: 38-44. PMID: 33681646
    3. 灵活的化学计量:对KCNQ2和KCNQ3相关神经发育障碍的影响。  |  Springer, K., et al. 2021. Dev Neurosci. 43: 191-200. PMID: 33794528
    4. KCNQ2基因突变与新生儿癫痫。  |  García Castellanos, MT., et al. 2021. Med Clin (Barc). 157: 589-590. PMID: 33962768
    5. KCNQ2和KCNQ5形成异构体通道,与KCNQ3无关。  |  Soh, H., et al. 2022. Proc Natl Acad Sci U S A. 119: e2117640119. PMID: 35320039
    6. 吡哆醇反应性KCNQ2癫痫性脑病:其他病例和文献综述。  |  Chen, J., et al. 2022. Mol Genet Genomic Med. 10: e2024. PMID: 35906921
    7. KCNQ2 脑病和对 5'-磷酸吡哆醛的反应性  |  Chow, CK., et al. 2023. J Pediatr Genet. 12: 90-94. PMID: 36684546
    8. KCNQ2相关发育性癫痫性脑病的临床分析和功能特征。  |  Ye, J., et al. 2023. Front Mol Neurosci. 16: 1205265. PMID: 37497102
    9. KCNQ2/3功能增强变异与细胞兴奋性:CA1与L2/3锥体神经元的不同影响。  |  Varghese, N., et al. 2023. J Neurosci. 43: 6479-6494. PMID: 37607817
    10. 直接打开KCNQ2通道的小分子激活机制。  |  Zhang, S., et al. 2024. Nat Chem Biol. 20: 847-856. PMID: 38167918

    订购信息

    产品名称产品编号规格价格数量收藏夹

    KCNQ2 抗体 (E-6)

    sc-365114
    200 µg/ml
    RMB2377.00

    I need to use an antibody to detect the protein in samples of avian origin. Do you know if sc-365114: KCNQ2 (E-6) mouse monoclonal antibody will work?

    Asked by: DefinitelyNotMatt
    Please contact our Technical Service Department and we would be happy to perform sequence analysis and review our data to answer any questions you may have about additional species reactivity.
    Answered by: Technical Support
    Date published: 2017-03-06
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    Rated 4 out of 5 by from Strong bands on western blotStrong bands on western blot, CHO cells or native tissue.
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    Rated 1 out of 5 by from Did not work in tissue after methanol fixationDid not work in tissue after methanol fixation
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    Rated 5 out of 5 by from Excellent results in Western BlotExcellent results in Western Blot -SCBT QC
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